[An atypical form of neurosarcoidosis].
La Revue de Médecine Interne. 2013-12-01; 34(12): 776-779
DOI: 10.1016/j.revmed.2013.02.035
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1. Rev Med Interne. 2013 Dec;34(12):776-9. doi: 10.1016/j.revmed.2013.02.035. Epub
2013 Nov 4.
[An atypical form of neurosarcoidosis].
[Article in French]
Quenardelle V(1), Benmekhbi M, Aupy J, Dalvit C, Hirsch E, Benoilid A.
Author information:
(1)Service de neurologie, CHU de Strasbourg, 1, avenue Molière, 67098 Strasbourg,
France.
INTRODUCTION: Nervous system involvement occurs in 5 to 15% of the patients with
sarcoidosis. Neurosarcoidosis remains very difficult to diagnose because clinical
presentation and imaging characteristics lack specificity.
OBSERVATION: We report a 26-year-old man who gradually developed headaches,
memory disturbance and epilepsy. CT-scan and MRI showed a temporal-parietal
cystic mass, secondary to a rare and focal form of hydrocephalus, called « trapped
temporal horn » revealing neurosarcoidosis.
CONCLUSION: The « entrapped temporal horn » is due to an obstacle on the
cerebrospinal fluid pathway at the trigone of the lateral ventricle that seals
off the temporal horn and the choroid plexus from the rest of the ventricular
system. The obstacle is related to the granulomatous tissue of sarcoidosis.
Therefore, the « trapped temporal horn » acts as a space occupying process, causing
headaches, memory pain, hemiparesis, homonymous hemianopsia, and requires
medico-surgical management.
Copyright © 2013 Société nationale française de médecine interne (SNFMI).
Published by Elsevier SAS. All rights reserved.
DOI: 10.1016/j.revmed.2013.02.035
PMID: 24200098 [Indexed for MEDLINE]